CASE REPORT
Characteristics of patients with blastemal-type Wilms’ tumour
1
Doctoral School, Department of Pediatric Hematology and Oncology, Faculty of Medical Sciences in Zabrze, Medical University of Silesia in Katowice, Poland
2
Students’ Scientific Association, Department of Pediatric Hematology and Oncology, Faculty of Medical Sciences in Zabrze, Medical University of Silesia in Katowice, Poland
3
Department of Pediatric Hematology and Oncology, Faculty of Medical Sciences in Zabrze, Medical University of Silesia in Katowice, Poland
Submission date: 2021-02-23
Final revision date: 2021-04-15
Acceptance date: 2021-05-05
Publication date: 2021-07-01
Pediatr Pol 2021;96(2):134-138
KEYWORDS
TOPICS
ABSTRACT
Wilms’ tumour (nephroblastoma) is the most common malignant tumour of kidney in children and one of the 2 most common solid tumours located outside of the central nervous system. Nephroblastoma has a very good prognosis, but some histological types like blastemal-type require qualification to a high-risk group and intensification of treatment. We present the cases of 3 children diagnosed with nephroblastoma, blastemal-type. The first girl’s treatment was unsuccessful, as there were 4 cancer recurrences. The second girl had primarily metachronous form of nephroblastoma, but during recurrence the blastemal-type was diagnosed. Despite intensive treatment, it ended with failure. The third girl had a tumour in the left kidney, which was transformed from the bilateral nephroblastomatosis. She remains in remission; the therapy ended on February 2018.
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